What it is
A vestibular schwannoma is a benign tumor that arises from the Schwann cells insulating the eighth cranial nerve, which carries hearing and balance information from the inner ear to the brain. Most arise from the vestibular (balance) division of that nerve — the origin of the name — though some involve the cochlear (hearing) division. Because the nerve travels through a narrow bony channel and passes near the facial nerve, even a small tumor can produce noticeable symptoms.
Most vestibular schwannomas grow slowly, and some do not grow at all over years of observation. They occur sporadically in the large majority of cases. Tumors on both sides are uncommon and raise the possibility of an underlying genetic condition, which changes how the tumor is evaluated and followed.
Symptoms
The most common presentation is gradual hearing loss in one ear, often noticed first on the telephone or in a noisy room. Other symptoms include:
- Asymmetric hearing loss — hearing that is measurably worse in one ear
- Tinnitus — ringing, hissing, or buzzing, usually on the affected side
- Imbalance or unsteadiness, more often a vague sense of being off than true spinning vertigo
- A feeling of fullness in the affected ear
- Facial numbness or tingling, which suggests a larger tumor contacting the trigeminal nerve
- Facial weakness, which is uncommon at presentation and generally indicates a larger tumor
Sudden hearing loss in one ear can also be a presenting sign. Because the symptoms develop gradually and are easy to attribute to age or wax, many vestibular schwannomas are found only after an asymmetry shows up on a hearing test.
How it is diagnosed
Evaluation usually begins with a complete audiogram, which documents the pattern and degree of hearing loss and compares the two ears. Asymmetric sensorineural hearing loss is the finding that most often prompts imaging.
MRI with gadolinium contrast is the definitive test. It shows the tumor, its size, and its relationship to the internal auditory canal, the brainstem, and the surrounding cranial nerves. Tumors too small to be seen on a standard CT scan are readily visible on a dedicated MRI protocol.
Additional testing — balance function studies, or a full cranial nerve assessment — may be added depending on the size of the tumor and the symptoms.
Management options
There are three established approaches, and the best choice depends on tumor size, growth on serial imaging, hearing status, age, overall health, and personal preference.
Observation. Serial MRI scans and hearing tests track the tumor over time. This is frequently the right first step for small tumors that are causing limited symptoms, since a substantial proportion grow slowly or not at all. Observation is an active strategy, not a decision to do nothing — the point is to intervene if and when the tumor demonstrates that it needs treatment.
Stereotactic radiosurgery. Focused radiation delivered in a single session or a small number of sessions, with the goal of stopping growth rather than removing the tumor. It is most often used for small and medium tumors. See Gamma Knife stereotactic radiosurgery for more detail.
Microsurgical removal. Surgery to remove the tumor, approached through the mastoid bone, behind the ear, or above the ear canal depending on tumor size, position, and whether hearing preservation is a realistic goal. Larger tumors, tumors compressing the brainstem, and tumors that continue to grow after other treatment are the usual indications. Facial nerve function is monitored throughout the operation.
For patients who lose hearing on the affected side, several rehabilitation options exist, including osseointegrated hearing devices and, in selected cases, cochlear implantation.
What to expect at your visit
Bring any prior hearing tests and imaging, including the actual MRI images rather than only the report if you can obtain them. A typical consultation includes a review of your history and symptoms, an ear examination, a cranial nerve examination, and a detailed discussion of the imaging. The goal of the first visit is a shared understanding of what the tumor is doing and what the realistic options are — not necessarily an immediate decision.